Julien Ochala
Associate Professor - Promotion Programme
- Published
The effects of resistance exercise training on mitochondrial myopathy patients
Di Leo, V., Newman, J., Lawless, C., Robertson, F., Levy, Y., Ochala, Julien, Pickett, S., Hudson, G., Gorman, G., Tuppen, H., Vincent, A. & Russell, O., 2022, In: Neuromuscular Disorders. 32, p. S72-S72 FP.16.Research output: Contribution to journal › Conference abstract in journal › Research
- Published
The fraction of strongly bound cross-bridges is increased in mice that carry the myopathy-linked myosin heavy chain mutation MYH4L342Q
Lindqvist, J., Iwamoto, H., Blanco, G. & Ochala, Julien, May 2013, In: DMM Disease Models and Mechanisms. 6, 3, p. 834-840 7 p.Research output: Contribution to journal › Journal article › Research › peer-review
- Published
The influence of ageing on the force-velocity-power characteristics of human elbow flexor muscles
Valour, D., Ochala, Julien, Ballay, Y. & Pousson, M., 1 Apr 2003, In: Experimental Gerontology. 38, 4, p. 387-395 9 p.Research output: Contribution to journal › Journal article › Research › peer-review
- Published
Thick and Thin Filament Proteins: Acquired and Hereditary Sarcomeric Protein Diseases
Ochala, Julien & Larsson, L., 18 Jul 2012, Muscle: Fundamental Biology and Mechanisms of Disease. Elsevier, Vol. 1-2. p. 1023-1030 8 p.Research output: Chapter in Book/Report/Conference proceeding › Book chapter › Research › peer-review
- Published
Thick and thin filament proteins: Acquired and hereditary sarcomeric protein diseases
Ochala, Julien & Larsson, L., 2012, Muscle. Elsevier Science Inc., Vol. 2. p. 1023-1030 8 p.Research output: Chapter in Book/Report/Conference proceeding › Book chapter › Research › peer-review
Thin filament proteins mutations associated with skeletal myopathies: Defective regulation of muscle contraction
Ochala, Julien, 2008, In: Journal of Molecular Medicine. 86, 11, p. 1197-1204 8 p.Research output: Contribution to journal › Review › Research › peer-review
Tropomodulin 1 directly controls thin filament length in both wild-type and tropomodulin 4-deficient skeletal muscle
Gokhin, D. S., Ochala, Julien, Domenighetti, A. A. & Fowler, V. M., 15 Dec 2015, In: Development (Cambridge, England). 142, 24, p. 4351-62 12 p.Research output: Contribution to journal › Journal article › Research › peer-review
- Published
Using nuclear envelope mutations to explore age-related skeletal muscle weakness
Battey, E., Stroud, M. J. & Ochala, Julien, 28 Aug 2020, In: Clinical Science. 134, 16, p. 2177-2187 11 p.Research output: Contribution to journal › Journal article › Research › peer-review
- Published
X-ray recordings reveal how a human disease-linked skeletal muscle α-actin mutation leads to contractile dysfunction
Ochala, Julien, Ravenscroft, G., McNamara, E., Nowak, K. J. & Iwamoto, H., Dec 2015, In: Journal of Structural Biology. 192, 3, p. 331-335 5 p.Research output: Contribution to journal › Journal article › Research › peer-review
- Published
rAAV-related therapy fully rescues myonuclear and myofilament function in X-linked myotubular myopathy
Ross, J. A., Tasfaout, H., Levy, Y., Morgan, J., Cowling, B. S., Laporte, J., Zanoteli, E., Romero, N. B., Lowe, D. A., Jungbluth, H., Lawlor, M. W., Mack, D. L. & Ochala, Julien, 19 Oct 2020, In: Acta Neuropathologica Communications. 8, 1, 167.Research output: Contribution to journal › Journal article › Research › peer-review
ID: 240294914
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104
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Impairments in contractility and cytoskeletal organisation cause nuclear defects in nemaline myopathy
Research output: Contribution to journal › Journal article › Research › peer-review
Published -
59
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Myofibre hyper-contractility in horses expressing the myosin heavy chain myopathy mutation, myh1e321g
Research output: Contribution to journal › Journal article › Research › peer-review
Published -
29
downloads
Using nuclear envelope mutations to explore age-related skeletal muscle weakness
Research output: Contribution to journal › Journal article › Research › peer-review
Published