Julien Ochala
Associate Professor - Promotion Programme
- Published
Mechanisms underlying the sparing of masticatory versus limb muscle function in an experimental critical illness model
Aare, S., Ochala, Julien, Norman, H. S., Radell, P., Eriksson, L. I., Göransson, H., Chen, Y. W., Hoffman, E. P. & Larsson, L., Dec 2011, In: Physiological Genomics. 43, 24, p. 1334-1350 17 p.Research output: Contribution to journal › Journal article › Research › peer-review
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Binding pocket dynamics along the recovery stroke of human β-cardiac myosin
Akter, F., Ochala, Julien & Fornili, A., 2023, In: PLOS Computational Biology. 19, 5, 14 p., e1011099.Research output: Contribution to journal › Journal article › Research › peer-review
- Published
Comparative study of binding pocket structure and dynamics in cardiac and skeletal myosin
Antonovic, A. K., Ochala, Julien & Fornili, A., 2023, In: Biophysical Journal. 122, 1, p. 54-62Research output: Contribution to journal › Journal article › Research › peer-review
- Published
Muscle paralysis and myosin loss in a patient with cancer cachexia
Banduseela, V., Ochala, Julien, Lamberg, K., Kalimo, H. & Larsson, L., Dec 2007, In: Acta Myologica. 26, 3, p. 136-144 9 p.Research output: Contribution to journal › Journal article › Research › peer-review
- Published
Gene expression and muscle fiber function in a porcine ICU model
Banduseela, V. C., Ochala, Julien, Chen, Y. W., Göransson, H., Norman, H., Radell, P., Eriksson, L. I., Hoffman, E. P. & Larsson, L., Nov 2009, In: Physiological Genomics. 39, 3, p. 141-159 19 p.Research output: Contribution to journal › Journal article › Research › peer-review
- E-pub ahead of print
Myonuclear alterations associated with exercise are independent of age in humans
Battey, E., Ross, J. A., Hoang, A., Wilson, D. G. S., Han, Y., Levy, Y., Pollock, R. D., Kalakoutis, M., Pugh, J. N., Close, G. L., Ellison-Hughes, G. M., Lazarus, N. R., Iskratsch, T., Harridge, S. D. R., Ochala, Julien & Stroud, M. J., 2024, (E-pub ahead of print) In: Journal of Physiology.Research output: Contribution to journal › Journal article › Research › peer-review
- Published
Using nuclear envelope mutations to explore age-related skeletal muscle weakness
Battey, E., Stroud, M. J. & Ochala, Julien, 28 Aug 2020, In: Clinical Science. 134, 16, p. 2177-2187 11 p.Research output: Contribution to journal › Journal article › Research › peer-review
- Published
Muscle fibre size and myonuclear positioning in trained and aged humans
Battey, E., Levy, Y., Pollock, R. D., Pugh, J. N., Close, G. L., Kalakoutis, M., Lazarus, N. R., Harridge, S. D. R., Ochala, Julien & Stroud, M. J., 2024, In: Experimental Physiology. 109, 4, p. 549-561Research output: Contribution to journal › Journal article › Research › peer-review
- Published
PGC-1α regulates myonuclear accretion after moderate endurance training
Battey, E., Furrer, R., Ross, J., Handschin, C., Ochala, Julien & Stroud, M. J., 2022, In: Journal of Cellular Physiology. 237, 1, p. 696-705Research output: Contribution to journal › Journal article › Research › peer-review
Effect of PGC1-beta ablation on myonuclear organisation
Beedour, R., Ross, J. A., Levy, Y. & Ochala, Julien, 1 Dec 2019, In: Journal of Muscle Research and Cell Motility. 40, 3-4, p. 335-341 7 p.Research output: Contribution to journal › Journal article › Research › peer-review
Reducing dynamin 2 (DNM2) rescues DNM2-related dominant centronuclear myopathy
Buono, S., Ross, J. A., Tasfaout, H., Levy, Y., Kretz, C., Tayefeh, L., Matson, J., Guo, S., Kessler, P., Monia, B. P., Bitoun, M., Ochala, Julien, Laporte, J. & Cowling, B. S., 23 Oct 2018, In: Proceedings of the National Academy of Sciences of the United States of America. 115, 43, p. 11066-11071 6 p.Research output: Contribution to journal › Journal article › Research › peer-review
- Published
A Laing distal myopathy-associated proline substitution in the β-myosin rod perturbs myosin cross-bridging activity
Buvoli, M., Wilson, G. C., Buvoli, A., Gugel, J. F., Hau, A., Bönnemann, C. G., Paradas, C., Ryba, D. M., Woulfe, K. C., Walker, L. A., Buvoli, T., Ochala, Julien & Leinwand, L. A., 2024, In: The Journal of Clinical Investigation. 134, 9, 16 p., :e172599.Research output: Contribution to journal › Journal article › Research › peer-review
- Published
Human skeletal myopathy myosin mutations disrupt myosin head sequestration
Carrington, G., Hau, A., Kosta, S., Dugdale, H. F., Muntoni, F., D’Amico, A., Van den Bergh, P., Romero, N. B., Malfatti, E., Vilchez, J. J., Oldfors, A., Pajusalu, S., Õunap, K., Giralt-Pujol, M., Zanoteli, E., Campbell, K. S., Iwamoto, H., Peckham, M. & Ochala, Julien, 2023, In: JCI insight. 8, 21, p. 1-19 e172322.Research output: Contribution to journal › Journal article › Research › peer-review
- Published
Myopathy-inducing mutation H40Y in ACTA1 hampers actin filament structure and function
Chan, C., Fan, J., Messer, A. E., Marston, S. B., Iwamoto, H. & Ochala, Julien, 1 Aug 2016, In: Biochimica et Biophysica Acta - Molecular Basis of Disease. 1862, 8, p. 1453-1458 6 p.Research output: Contribution to journal › Journal article › Research › peer-review
- Published
Nuclear numbers in syncytial muscle fibers promote size but limit the development of larger myonuclear domains
Cramer, A. A. W., Prasad, V., Eftestøl, E., Song, T., Hansson, K. A., Dugdale, H. F., Sadayappan, S., Ochala, Julien, Gundersen, K. & Millay, D. P., 2020, In: Nature Communications. 11, 1, 14 p., 6287.Research output: Contribution to journal › Journal article › Research › peer-review
- Published
Activation of eIF4E-binding-protein-1 rescues mTORC1-induced sarcopenia by expanding lysosomal degradation capacity
Crombie, E. M., Kim, S., Adamson, S., Dong, H., Lu, T. C., Wu, Y., Wu, Y., Levy, Y., Stimple, N., Lam, W. M. R., Hey, H. W. D., Withers, D. J., Hsu, A. L., Bay, B. H., Ochala, Julien & Tsai, S. Y., 2023, In: Journal of Cachexia, Sarcopenia and Muscle. 14, p. 198–213Research output: Contribution to journal › Journal article › Research › peer-review
- Published
The effects of resistance exercise training on mitochondrial myopathy patients
Di Leo, V., Newman, J., Lawless, C., Robertson, F., Levy, Y., Ochala, Julien, Pickett, S., Hudson, G., Gorman, G., Tuppen, H., Vincent, A. & Russell, O., 2022, In: Neuromuscular Disorders. 32, p. S72-S72 FP.16.Research output: Contribution to journal › Conference abstract in journal › Research
- Published
Can we talk about myoblast fusion?
Dugdale, H. F. & Ochala, Julien, 2021, In: American Journal of Physiology - Cell Physiology. 321, 3, p. C504-C506Research output: Contribution to journal › Review › Research › peer-review
- Published
Aberrant myonuclear domains and impaired myofiber contractility despite marked hypertrophy in MYMK-related, Carey-Fineman-Ziter Syndrome
Dugdale, H. F., Levy, Y., Jungbluth, H., Oldfors, A. & Ochala, Julien, 2024, In: Acta Neuropathologica Communications. 12, 1, 80.Research output: Contribution to journal › Journal article › Research › peer-review
Molecular consequences of the myopathy-related D286G mutation on actin function
Fan, J., Chan, C., McNamara, E. L., Nowak, K. J., Iwamoto, H. & Ochala, Julien, 1 Dec 2018, In: Frontiers in Physiology. 9, 1756.Research output: Contribution to journal › Journal article › Research › peer-review
- Published
Early clinical and pre-clinical therapy development in Nemaline myopathy
Fisher, G., Mackels, L., Markati, T., Sarkozy, A., Ochala, Julien, Jungbluth, H., Ramdas, S. & Servais, L., 28 Dec 2022, In: Expert Opinion On Therapeutic Targets. 26, 10, p. 853–867Research output: Contribution to journal › Review › Research › peer-review
- Published
Skeletal Muscle: A Brief Review of Structure and Function
Frontera, W. R. & Ochala, Julien, 4 Mar 2015, In: Behavior Genetics. 45, 2, p. 183-195 13 p.Research output: Contribution to journal › Review › Research › peer-review
Tropomodulin 1 directly controls thin filament length in both wild-type and tropomodulin 4-deficient skeletal muscle
Gokhin, D. S., Ochala, Julien, Domenighetti, A. A. & Fowler, V. M., 15 Dec 2015, In: Development (Cambridge, England). 142, 24, p. 4351-62 12 p.Research output: Contribution to journal › Journal article › Research › peer-review
- Published
Slow myosin heavy chain 1 is required for slow myofibril and muscle fibre growth but not for myofibril initiation
Hau, H. T. A., Kelu, J. J., Ochala, Julien & Hughes, S. M., Jul 2023, In: Developmental Biology. 499, p. 47-58 12 p.Research output: Contribution to journal › Journal article › Research › peer-review
- Published
Correction: Impaired adaptive response to mechanical overloading in dystrophic skeletal muscle (PLoS ONE)
Joanne, P., Hourdé, C., Ochala, Julien, Caudéran, Y., Medja, F., Vignaud, A., Mouisel, E., Hadj-Said, W., Arandel, L., Garcia, L., Goyenvalle, A., Mounier, R., Zibroba, D., Sakamato, K., Butler-Browne, G., Agbulut, O. & Ferry, A., 27 Jun 2013, In: PLoS ONE. 8, 6Research output: Contribution to journal › Comment/debate › Research › peer-review
ID: 240294914
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104
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Impairments in contractility and cytoskeletal organisation cause nuclear defects in nemaline myopathy
Research output: Contribution to journal › Journal article › Research › peer-review
Published -
60
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Myofibre hyper-contractility in horses expressing the myosin heavy chain myopathy mutation, myh1e321g
Research output: Contribution to journal › Journal article › Research › peer-review
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30
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Using nuclear envelope mutations to explore age-related skeletal muscle weakness
Research output: Contribution to journal › Journal article › Research › peer-review
Published